What is a Meningoencephalocele?
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Meningoencephalocele is a rare congenital anomaly that is characterized by herniation of brain tissue through a defect in skull. Generally, it could be divided by anatomical location of defect to occipital and frontoethmoidal. The exact etiology of this condition is unknown but many theories have been postulated.
What is Gliocele?
Gliocele : Glial-lined cyst containing CSF. • May also be categorized by location of bony defect.
What is cranium bifidum?
Cranium bifidum is an abnormal osseous defect of the calvarium through which herniation of meninges and brain tissue may occur. It occurs with midline malformations such as myelomeningocele, meningoencephalocele or dermal sinus [1].
Is encephalocele a rare disease?
Encephalocele is a rare type of birth defect of the neural tube that affects the brain. The neural tube is a narrow channel that folds and closes during the third and fourth weeks of pregnancy to form the brain and spinal cord.
Is encephalocele fatal?
Fetuses with an encephalocele are likely to die before birth. Approximately 21 percent, or 1 in 5, are born alive. Of those born alive, only 50 percent will survive.
What is occipital encephalocele?
Occipital encephalocele (OE) are the most common form of this congenital disorder and are manifested as a swelling of different sizes over the occipital bone in the midline. Proper diagnosis and treatment is highly important in the management of this congenital malformation of brain.
What is occipital Meningocele?
Definition. A herniation of meninges through a congenital bone defect in the skull in the occipital region. [ from HPO]
What causes Hydranencephaly?
Hydranencephaly is considered to be an extreme form of porencephaly (a rare disorder characterized by a cyst or cavity in the cerebral hemispheres) and may be caused by vascular infections or traumatic disorders after the 12th week of pregnancy.
How common is spina bifida occulta?
Spina bifida occulta is when a baby’s backbone (spine) does not fully form during pregnancy. The baby is born with a small gap in the bones of the spine. The condition is common and happens in about 1 out of 10 people. Usually, it causes no health problems.
Can a baby survive encephalocele?
Babies with an encephalocele at the back of the head have a 55 percent survival rate. Long-term prognosis for survival becomes less likely if there are other complications, such as associated defects or syndromes or if brain tissue protrudes into the sac.
Can encephalocele be cured?
Treatment. Encephalocele is treated with surgery to place the protruding part of the brain and the membranes covering it back into the skull and close the opening in the skull. However, neurologic problems caused by the encephalocele will still be present. Long-term treatment depends on the child’s condition.
Is encephalocele serious?
When the neural tube does not close, it can cause a sac-like bulge with brain tissue and spinal fluid that pokes through the skull. An encephalocele can be life-threatening.